Keywords
childhood
neoplasia
pediatrics
tumor
How to Cite
Abstract
Introduction. Adrenal cortex tumors in pediatric patients are rare and constitute less than 0.2% of all malignancies in childhood. Case development. We here present a case of an 11-month-old girl who was admitted to the Pediatric Oncology Department due to a Cushingoid appearance, severe arterial hypertension, intense virilization, high body weight, and recurrent oropharyngeal candidiasis. The imaging tests and hormonal study performed confirmed the diagnosis of a functioning adrenal tumor, with secondary Cushing’s syndrome and hyperaldosteronism. After an urgent surgical approach, hormonal levels normalized, improving all the symptoms and signs presented by the patient. Conclusions. Adrenocortical tumors in children are very rare but highly aggressive, so early diagnosis and urgent treatment are essential to prevent their progression and improve the quality of life of patients.
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